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04_Summary
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49_porphyria
49_porphyria
9 items under this folder.
Aug 14, 2026
ๅผ่จ (Introduction)
็ฎ่็ง
metabolic_and_systemic_diseases
porphyria
key_features
heme_biosynthesis
photosensitivity
Aug 14, 2026
ๅ่จ (Introduction)
็ฎ่็ง
metabolic_and_systemic_diseases
porphyria
introduction
heme_biosynthetic_pathway
classification
Aug 14, 2026
ๆญทๅฒ (History)
็ฎ่็ง
metabolic_and_systemic_diseases
porphyria
history
Aug 14, 2026
ๆต่ก็ ๅญธ (Epidemiology)
็ฎ่็ง
metabolic_and_systemic_diseases
porphyria
epidemiology
prevalence
Aug 14, 2026
่ด็ ๆฉ่ฝ (Pathogenesis)
็ฎ่็ง
metabolic_and_systemic_diseases
porphyria
pathogenesis
soret_band
reactive_oxygen_species
acute_porphyric_attack
Aug 14, 2026
่จๅบ่ๅฏฆ้ฉๅฎคๆชขๆฅ (Clinical and Laboratory Investigation)
็ฎ่็ง
metabolic_and_systemic_diseases
porphyria
diagnosis
laboratory_investigation
genetic_testing
Aug 14, 2026
้ๆฅๆง็ดซ่ณช็ (The Non-Acute Porphyrias)
็ฎ่็ง
metabolic_and_systemic_diseases
porphyria
non_acute_porphyrias
porphyria_cutanea_tarda
erythropoietic_protoporphyria
congenital_erythropoietic_porphyria
pseudoporphyria
photosensitivity
phlebotomy
afamelanotide
Aug 14, 2026
ๆฅๆง็ดซ่ณช็ (The Acute Porphyrias)
็ฎ่็ง
metabolic_and_systemic_diseases
porphyria
acute_porphyrias
acute_intermittent_porphyria
variegate_porphyria
hereditary_coproporphyria
heme_arginate
givosiran
Aug 14, 2026
้้ (Appendix)
็ฎ่็ง
metabolic_and_systemic_diseases
porphyria
appendix
reference_laboratories
givosiran